Korean J Gastroenterol.
1999 May;33(5):708-712.
A Case of Sclerosing Mediastinitis Presenting as Esophageal Stricture
Abstract
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Sclerosing mediastinitis is a rare condition in which fibrosis and sclerosis of the mediastinum cause obstruction to intrathoracic organs. In nearly 80% of the reported cases, sclerosing mediastinitis was idiopathic, but it could occur secondarily due to histoplasmosis, tuberculosis, sarcoidosis, or drugs like methysergide. An idiopathic proliferation of dense fibrous tissue can cause mediastinal fibrosis retroperitoneal fibrosis, sclerosing mesenteritis, systemic sclerosis and Riedel' s thyroiditis. The combined mediastinal and retroperitoneal fibrosis is a rare, localized manifestation of the idiopathic systemic sclerosing disease. We report a case presenting as an esophageal stricture due to sclerosing mediastinitis associated with retroperitoneal fibrosis.