Korean Circ J.  2002 Sep;32(9):825-828. 10.4070/kcj.2002.32.9.825.

A Case of Intravenous Leiomyomatosis Extending into the Right Atrium

Affiliations
  • 1Department of Internal Medicine, Gachon Medical School Gil Medical Center, Incheon, Korea.
  • 2Department of Thoracic and Cardiovascular Surgery, Gachon Medical School Gil Medical Center, Incheon, Korea.
  • 3Department of General Surgery, Gachon Medical School Gil Medical Center, Incheon, Korea.

Abstract

Intravenous leiomyomatosis is a rare entity of benign smooth muscle invading into the lumen of veins. We describe a case of intracardiac leiomyomatosis originating from the right gonadal vein, growing in the inferior vena cava, and extending into the right atrium. A 54 years old woman presented with chest discomfort and syncope four years after the removal of an uterine leiomyoma. The tumor was successfully removed in a two-staged operation using total circulatory arrest with a cardiopulmonary bypass, which proved to be a histologically benign leiomyoma. Although these tumors are histologically benign, they sometimes extend into the cardiac cavity and can cause sudden death due to their incarceration into the atrioventircular orifice. We report this rare case with a review of the literature.

Keyword

Leiomyomatosis; Heart atrium

MeSH Terms

Cardiopulmonary Bypass
Death, Sudden
Female
Gonads
Heart Atria*
Humans
Leiomyoma
Leiomyomatosis*
Middle Aged
Muscle, Smooth
Syncope
Thorax
Veins
Vena Cava, Inferior
Full Text Links
  • KCJ
Actions
Cited
CITED
export Copy
Close
Share
  • Twitter
  • Facebook
Similar articles
Copyright © 2024 by Korean Association of Medical Journal Editors. All rights reserved.     E-mail: koreamed@kamje.or.kr