J Rheum Dis.  2012 Feb;19(1):39-42. 10.4078/jrd.2012.19.1.39.

Transverse Myelitis in Patient with Behcet's Disease

• Bae HJ
• Jung CG
• Lee JH
• Kim TY
• Lee S
• Chae JN
• Chang HW
• Yi HA
• Kim SH

• KMID: 2223118
• DOI: http://doi.org/10.4078/jrd.2012.19.1.39

Abstract

Behcet's disease (BD) is a multisystem disorder presenting recurrent oral and genital ulcerations as well as ocular lesions, involving the nervous system in a subgroup of patients. BD develops at a young age and is frequently presented with an acute or subacute brainstem syndrome or hemiparesis, as well as with other various neurological manifestations, the syndrome is often included in the differential diagnosis of multiple sclerosis, stroke of the young adult, and other neurological disorders. Transverse myelitis (TM) is a clinical syndrome in which an immune-mediated process causes neural injury to the spinal cord, resulting in varying degrees of weakness, sensory alterations and autonomic dysfunction. Spinal Neuro-behcet's disease is rare case. We reported a 33-year old man who had been treated for BD for 3 years.

Keyword

Behcet's disease; Transverse myelitis

MeSH Terms

Brain Stem
Diagnosis, Differential
Humans
Multiple Sclerosis
Myelitis, Transverse
Nervous System
Nervous System Diseases
Neurologic Manifestations
Paresis
Spinal Cord
Stroke
Ulcer
Young Adult

Figure

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  Figure 1 Axial and sagittal T2 weighted image (T2WI) of thoracic spine (T-spine) revealed high signal intensity (arrows) in T6 spinal cord.

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  Figure 2 Follow up axial and sagittal T2WI of T-spine revealed a high signal intensity in T6 spinal cord.

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