J Rheum Dis.  2013 Oct;20(5):332-335. 10.4078/jrd.2013.20.5.332.

A Case of Lung Involvement Associated with Juvenile Idiopathic Arthritis

• Koo CM
• Choi SY
• Ahn JG
• Kim KH
• Kim DS

• KMID: 2223012
• DOI: http://doi.org/10.4078/jrd.2013.20.5.332

Abstract

Juvenile idiopathic arthritis (JIA) can develop extra-articular manifestations, including growth retardation, osteopenia and chronic uveitis. However, pleuropulmonary involvement is rare. Approximately 40% of patients with JIA have abnormal pulmonary function tests without pulmonary symptoms, with the commonest abnormality in carbon monoxide diffusing capacity, but clinically evident pulmonary parenchymal disease in JIA is extremely uncommon. We describe a 15-year-old male with JIA who presented with dyspnea due to interstitial lung disease.

Keyword

Arthritis; Juvenile rheumatoid; Lung disease

MeSH Terms

Adolescent
Arthritis
Arthritis, Juvenile Rheumatoid*
Bone Diseases, Metabolic
Carbon Monoxide
Dyspnea
Humans
Lung Diseases
Lung Diseases, Interstitial
Lung*
Male
Respiratory Function Tests
Uveitis
Carbon Monoxide

Figure

• 

  Figure 1. Chest PA shows pneumomediastinum (white arrow head), right pleural effusion (black arrow) and honeycombing in Left Lower lobe (white arrow).

• 

  Figure 2. High resolution CT (HRCT) scan shows pneumomediastinum (black arrow), honeycombing, ground-glass opacity (white arrow), septal thickening and small nodules in both lung fields.

• 

  Figure 3. Followup High resolution CT (HRCT) scan shows decreased pneumomediastinum (black arrow) and slightly decreased honeycombing, ground-glass opacity (white arrow).

Reference

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