J Korean Pediatr Soc.
2001 Aug;44(8):954-958.
A Case of Acute Necrotizing Encephalopathy
- Affiliations
-
- 1Department of Pediatrics, College of Medicine, Inje University, Seoul Paik Hospital, Seoul, Korea.
- 2Department of Pediatrics, College of Medicine, Inje University, Sang-Gye Paik Hospital, Seoul, Korea.
Abstract
- This disease predominantly affects infants and young children living in Japan and Taiwan, and manifests itself as acute encephalopathy following viral infections. The hallmark of this encephalopathy is multifocal, symmetric brain lesions affecting bilateral thalamus, brainstem tegmentum, cerebral periventricular white matter and cerebellar medulla, which can be visualized by computed tomography and magnetic resonance imaging. Both the gray and white matter are involved, with neuropathological evidence of local breakdown of the blood-brain barrier. The prognosis was poor in the 1980s, but has improved recently. A characteristic combination of focal neurologic signs is often recognized as the sequelae. We experienced a case of a 7-month-old male infant who had been transferred to our hospital for comatous mentality and clonic seizure of both arms and legs. We report this case with a review of the related literatures.
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