J Korean Neurosurg Soc.  2015 Feb;57(2):143-146. 10.3340/jkns.2015.57.2.143.

Globus Pallidus Interna Deep Brain Stimulation for Chorea-Acanthocytosis

Affiliations
  • 1Department of Neurology, Pusan National University School of Medicine, Busan, Korea.
  • 2Department of Neurosurgery, Pusan National University School of Medicine, Busan, Korea. drdwkang@gmail.com

Abstract

Chorea-acanthocytosis (ChAc) is a rare hereditary disorder characterized by involuntary choreiform movements and erythrocytic acanthocytosis. Pharmacotherapy for control of involuntary movements has generally been of limited benefit. Deep brain stimulation (DBS) has recently been used for treatment of some refractory cases of ChAc. We report here on the effect of bilateral high-frequency DBS of globus pallidus interna in a patient with ChAc.

Keyword

Chorea-acanthocytosis; Deep brain stimulation; Chorea; Globus pallidus

MeSH Terms

Abetalipoproteinemia
Chorea
Deep Brain Stimulation*
Drug Therapy
Dyskinesias
Globus Pallidus*
Humans
Neuroacanthocytosis*
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