J Korean Neurosurg Soc.  1979 Sep;8(2):431-438.

A Case of Diencephalic Syndrome

• Lee KC
• Rim CS
• Chu JW
• Lee HK

Abstract

Authors report a case of diencephalic syndrome which was observed in the patient with astrocytoma in the region of anterior hypothalamus and optic chiasm. An enlarged head, emaciation and hyperactive response were the symptoms. The subject, 8-month-old female infant, was bright and alert and had a history of failure to gain weight for months in spite of the fact that the child had eaten well. Skull X-rays showed no significant pathological findings but for enlarged head with suture separation. Conray ventriculography and CT scanning disclosed signs of presence of tumor in the suprasellar region. Craniotomy for removal of the tumor was followed by ventriculoperitoneal shunt.

MeSH Terms

Astrocytoma
Child
Craniotomy
Emaciation
Female
Head
Humans
Hypothalamus, Anterior
Infant
Optic Chiasm
Skull
Sutures
Tomography, X-Ray Computed
Ventriculoperitoneal Shunt