Ann Dermatol.  2011 Sep;23(Suppl 1):S53-S56. 10.5021/ad.2011.23.S1.S53.

Papular Elastorrhexis: A Case and Differential Diagnosis

• Choi Y
• Jin SY
• Lee JH
• Kwon HB
• Lee AY
• Lee SH

• KMID: 2156751
• DOI: http://doi.org/10.5021/ad.2011.23.S1.S53

Abstract

Papular elastorrhexis is a rare cutaneous disorder that occurs predominantly during adolescence. The disorder is characterized by asymptomatic indurated white or flesh papules showing decreased and fragmented elastic fibers in the dermis. We herein report on a 12-year-old girl with multiple asymptomatic white, nonfollicular, firm papules scattered on the extremities and trunk. Histological examination revealed focal areas showing increased layers of collagen fibers and decreased and fragmented elastic fibers in the upper dermis.

Keyword

Connective tissue nevus; Differential diagnosis; Papular elastorrhexis

MeSH Terms

Adolescent
Child
Collagen
Dermis
Diagnosis, Differential
Elastic Tissue
Extremities
Humans
Nevus
Collagen
Nevus

Figure

• 

  Fig. 1 Multiple asymptomatic discrete firm nonfollicular whitish papules on the extremities.

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  Fig. 2 (A) Increased layer of thin meshwork of collagen fibers in the upper dermis (H&E, ×100). (B) Decrease and fragmentation of elastic fibers in the upper dermis (Verhoeff's iron hematoxylin, ×100).

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