J Korean Ophthalmol Soc.  2002 Jan;43(1):213-218.

A Case of Subperiosteal Orbital Hematoma Associated with von Willebrand Disease

• Huh KC
• Kim YD

Abstract

PURPOSE: Subperiosteal orbital hematoma is rare, and most cases occur in children or young adults after direct facial or orbital trauma. Nontraumatic subperiosteal hemorrhage has been reported in association with systemic disease associated with leukemia, scurvy, sudden elevation of cranial venous pressure or venous congestion, and paranasal sinusitis. To our best knowledge, this is the first case of subperiosteal orbital hematoma associated with von Willebrand disease in Korea.
METHODS
A 30-year-old woman experienced a sudden onset of proptosis, diplopia and decreased visual acuity. Clinical features, orbital CT and MRI established the diagnosis of subperiosteal hematoma of the orbit. The patient was treated with superior orbitotomy with hematoma evacuation.
RESULTS
After the surgery, the patient's visual acuity completely recovered and proptosis disappeared. During follow-up periods, she was diagnosed to have von Willebrand disease.

Keyword

Proptosis; Subperiosteal orbital hematoma; Von Willebrand disease

MeSH Terms

Adult
Child
Diagnosis
Diplopia
Exophthalmos
Female
Follow-Up Studies
Hematoma*
Hemorrhage
Humans
Hyperemia
Korea
Leukemia
Magnetic Resonance Imaging
Orbit*
Scurvy
Sinusitis
Venous Pressure
Visual Acuity
von Willebrand Diseases*
Young Adult