J Korean Ophthalmol Soc.  2001 Aug;42(8):1232-1235.

A Case of Retinal Racemose Hemangioma

• Sang JH
• Kon LT
• Woo KJ

Abstract

PURPOSE: Racemose hemangiomas of the retina are rare developmental vascular anomalies with abnormal arteriovenous anastomoses. We report our observations of a retinal racemose hemangioma with marked dilation and tortuosity of the retinal vessels in the entire left retina.
METHODS
In a 9-year-old boy with loss of vision and mild esotropia who presented with hugely dilated and tortuous retinal vessels in left retina, we examined fundus, fluorescein angiography, cerebral angiography, brain CT and MRI.
RESULTS
Fundus and fluorescein angiography of the left eye showed marked dilation and tortuosity of the retinal vessels. Angiographic finding showed rapid filling of all vessels and no dye leakage. MRI finding revealed small tortuous vessels around left optic nerve, optic chiasm and tract. Brain CT and cerebral angiography showed nothing abnormal.

Keyword

Arteriovenous anastomosis; Retinal racemose hemangioma

MeSH Terms

Arteriovenous Anastomosis
Brain
Cerebral Angiography
Child
Esotropia
Fluorescein Angiography
Hemangioma*
Humans
Magnetic Resonance Imaging
Male
Optic Chiasm
Optic Nerve
Retina
Retinal Vessels
Retinaldehyde*
Retinaldehyde