J Korean Ophthalmol Soc.  2011 Nov;52(11):1381-1384.

A Case Report of Bilateral Retinal Racemose Hemangioma Restricted to Peripapillary Area

• Woo YJ
• Lee YH
• Yoon IN

Abstract

PURPOSE
The authors of the present case report observed a bilateral retinal racemose hemangioma which was located within the peripapillary area.
CASE SUMMARY
A 17-year-old man presented with floaters in both eyes. Fundus revealed tortuous and anastomosed retinal vasculature around the optic disc. In addition, fluorescein angiography showed a non-leaking retinal arteriovenous anastomosis. Seven years after the initial visit, vitreous hemorrhage occurred in the patient's left eye, and then 1 year later, subretinal hemorrhage was found in his left eye.
CONCLUSIONS
Because retinal racemose hemangioma can accompany vitreous hemorrhage and subretinal hemorrhage regardless of size, a routine periodic ophthalmic examination is recommended.

Keyword

Bilateral retinal racemose hemangioma; Complications

MeSH Terms

Adolescent
Arteriovenous Anastomosis
Eye
Fluorescein Angiography
Hemangioma
Hemorrhage
Humans
Retinaldehyde
Vitreous Hemorrhage
Retinaldehyde

Figure

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  Figure 1. Fluorescein angiograms of both eyes show rapid filling of vessels, no leakage and arteriovenous anastomosis.

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  Figure 2. Left two color fundus photographs show hemorrhagic complications of the left eye (A: vitreous hemorrhage, red arrow; B: subretinal hemorrhage, yellow arrow). Fluorescein angiogram (C) shows absent of new vessel or dye leakage.

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  Figure 3. Color fundus photographs of both eyes show tortuosity and concentration of the peripapillary retinal vessels, but there is no complication.

Reference

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