J Korean Radiol Soc.  2003 Dec;49(6):503-506. 10.3348/jkrs.2003.49.6.503.

Radiologic Findings of Cystic Fibrosis in a Korean Child at Follow Up Study: Case Report

• Jang IS
• Park CK
• Jeon SC
• Choi YW
• Park DW
• Kim Y
• Kim YS
• Ahn YH

• KMID: 2103752
• DOI: http://doi.org/10.3348/jkrs.2003.49.6.503

Abstract

Cystic fibrosis is a hereditary disease involving recessive transmission. The fundamental abnormality consists of the production of abnormal secretion from a variety of exocrine glands such as salivary and sweat glands and those of the pancreas, colon, and tracheobronchial trees. Cystic fibrosis is the most common lethal genetically transmitted disease among whites, but is uncommon in Asians, including Koreans. Although a case involving a Korean was reported in 1988, the focus was diagnosis rather than the radiological findings. In the case of cystic fibrosis we now describe, the focus is inverted: we enphasise the reported in 1988, focusing on radiologic findings.

Keyword

Fibrosis, cystic; Lung; Respiratory distress syndrome, in infants and children

MeSH Terms

Asian Continental Ancestry Group
Child*
Colon
Cystic Fibrosis*
Diagnosis
Exocrine Glands
Follow-Up Studies*
Genetic Diseases, Inborn
Humans
Lung
Pancreas
Sweat Glands