Korean J Anesthesiol.  2009 Nov;57(5):652-655. 10.4097/kjae.2009.57.5.652.

Anesthetic experience during reconstruction surgery of a chest wall defect in a patient with Poland syndrome: A case report

• Kim YH
• Kwon WJ
• Park SI

• KMID: 2092257
• DOI: http://doi.org/10.4097/kjae.2009.57.5.652

Abstract

Poland syndrome, which is characterized by an absence of pectoralis muscles and their innervated nerves, is marked by variable chest wall defects due to deficits of 2nd, 3rd, 4th, and 5th ribs and costal cartilage. Additionally, there are other reported combined anomalies of the heart, lung, kidney, ipsilateral hand and foot associated with the syndrome. The lung on the side with the thoracic deformity is more hypoplastic or smaller than the lung on the unaffected side, which can cause herniation of the lung or paradoxical ventilatory movement in severe cases, thereby increasing the risk of respiratory depression and hypoxemia. Patients may have profound lung complications due to depressed respiratory muscle function and exacerbation of the underlying chronic pulmonary disease during the perioperative period. These patients also show increased risk of malignant hyperthermia and therefore require careful attention during general anesthesia. We report here an anesthetic experience during reconstruction surgery of a chest wall defect in a male patient with Poland syndrome.

Keyword

Anesthesia; Chest wall defect; Poland syndrome

MeSH Terms

Anesthesia
Anesthesia, General
Anoxia
Cartilage
Congenital Abnormalities
Foot
Hand
Heart
Humans
Kidney
Lung
Lung Diseases
Male
Malignant Hyperthermia
Pectoralis Muscles
Perioperative Period
Poland
Poland Syndrome
Respiratory Insufficiency
Respiratory Muscles
Ribs
Thoracic Wall
Thorax