Korean J Pathol.
1999 Aug;33(8):631-635.
Primitive Neuroectodermal Tumor of the Ovary: A case report
- Affiliations
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- 1 Department of Clinical Pathology, College of Medicine, The Catholic University of Korea, Seoul 137-701, Korea.
Abstract
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Primitive neuroectodermal tumors (PNET) of the ovary are rare tumors with an
exclusive or almost exclusive malignant neuroectodermal composition, and are generally
regarded as a monodermal expression of an ovarian teratoma. The tumors are basically
identical with the lesions of the same name occuring typically in the central nervous
system of children. These tumors consist chiefly of undifferentiated small cells
resembling neuroblasts. There are also mature, well- differentiated neuroectodermal cells,
such as astrocytes and ependymal cells. We report a case of ovarian PNET with glial
and neuroblastic differentiation and focal teratomatous foci of non-neural tissue in a
17-year-old female.