Korean J Otolaryngol-Head Neck Surg.
2001 Dec;44(12):1342-1345.
A Case of Primitive Neuroectodermal Tumor in the Maxillary Sinus
- Affiliations
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- 1Department of Otorhinolaryngology-Head & Neck Surgery and 2; Anatomical Pathology, College of Medicine, Inje University, Pusan Paik Hospital, Pusan, Korea.
Abstract
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Primitive neuroectodermal tumor is a malignant small round cell tumor of presumed neural crest origin, which usually affect adolescents and children. Primitive neuroectodermal tumor occasionally occurs in the periphery. Peripheral primitive neuroectodermal tumor is usually located in the thoracopulmonary region and rarely found in the nasal cavity without intracranial metastasis. Due to frequent recurrence and early metastasis, prognosis of this tumor is bad and the treatment requires concomittant surgical removal, chemotheraphy, and radiation theraphy to ablate any residual disease. The authors experienced a case of primitive neuroectodermal tumor located in the maxillary sinus, so we report this case with a review of literature.