Korean J Anesthesiol.  2007 Dec;53(6):803-805. 10.4097/kjae.2007.53.6.803.

Intravenous Anesthesia in Spinal Muscular Atrophy: A case report

• Choi YH
• Gwak M
• Lee YK
• Lee YM
• Lee DH

• KMID: 1937353
• DOI: http://doi.org/10.4097/kjae.2007.53.6.803

Abstract

Spinal muscular atrophy (SMA) is a rare lower motor neuron disease in which anesthetic management is often difficult, because the patients usually have muscle weakness and hypersensitivity to muscle relaxants. We describe the anesthesia for a 8 year-old girl with type II SMA who presented for a lower lid epiblepharon repair. We chose to use intravenous anesthesia based on propofol and remifentanil without any muscle relaxants. The peri-operative course was completely uneventful. We consider that intravenous anesthesia without muscle relaxants could be a good anesthetic choice for a patient with SMA undering general anesthesia.

Keyword

intravenous anesthesia; muscle relaxants; spinal muscular atrophy

MeSH Terms

Anesthesia
Anesthesia, General
Anesthesia, Intravenous*
Child
Female
Humans
Hypersensitivity
Motor Neuron Disease
Muscle Weakness
Muscular Atrophy, Spinal*
Propofol
Propofol