J Korean Dent Soc Anesthesiol.  2004 Nov;4(2):100-103. 10.17245/jkdsa.2004.4.2.100.

General Anesthesia in a Child with Possible Spinal Muscular Atrophy Combined with Gingival Hyperplasia: A Case Report

• Seo KS
• Park CJ
• Kim HJ
• Yum KW

• KMID: 2345161
• DOI: http://doi.org/10.17245/jkdsa.2004.4.2.100

Abstract

Spinal muscular atrophies are inherited neurodegenerative disorders affecting anterior horn cells. There are various problems, especially weakness of respiratory muscle and abnormal reaction to muscle relaxants during the general anesthesia. And gingival hyperplasia can make the proper airway management difficult. Experience with anesthetic management in a patient with spinal muscular atrophy combined with gingival hyperplasia has been very rare. We report the anesthetic experience of a wheelchair-bound child, who underwent gingivectomy under general anesthesia. The child was safely managed with fibroscopic nasotracheal intubation under sevoflurane without muscle relaxants. Also, there was no deterioration of her underlying neurologic conditions.

Keyword

General anesthesia; Gingival hyperplasia; Neuromuscular disease; Sevoflurane

MeSH Terms

Airway Management
Anesthesia, General*
Anterior Horn Cells
Child*
Gingival Hyperplasia*
Gingivectomy
Humans
Intubation
Muscular Atrophy
Muscular Atrophy, Spinal*
Neurodegenerative Diseases
Neuromuscular Diseases
Respiratory Muscles