J Korean Neurosurg Soc.  2005 May;37(5):383-385.

Malignant Transformation of Fibrous Dysplasia on Anterior Skull Base

• Lee CJ
• Kim SM

Abstract

Malignant transformation of fibrous dysplasia is a rare condition and the incidence is estimated at 0.4% for fibrous dysplasia and 4% for Albright's syndrome. The authors did not find a reported case of malignant change at skull base around the orbit in the literature. We experienced a case of fibrous dysplasia, in which neurologic symptoms were aggravated due to malignant change around the orbit, and report its favorable outcome obtained with total surgical removal.

Keyword

Fibrous dysplasia; Skull base; Malignant transformation

MeSH Terms

Fibrous Dysplasia, Polyostotic
Incidence
Neurologic Manifestations
Orbit
Skull Base*
Skull*