J Korean Soc Radiol.
2021 Sep;82(5):1346-1351. 10.3348/jksr.2020.0206.
Osteosarcomatous Transformation in Mazabraud Syndrome: A Case Report
- Affiliations
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- 1Department of Radiology, Korea Cancer Center Hospital, Korea Institute of Radiological and Medical Sciences, Seoul, Korea
- KMID: 2520719
- DOI: http://doi.org/10.3348/jksr.2020.0206
Abstract
- Mazabraud syndrome is a rare benign disease that is accompanied by polyostotic fibrous dysplasia and intramuscular myxoma. Malignant transformation of fibrous dysplasia occurs in approximately 1% of cases. To date, only eight cases of malignant transformation, of fibrous dysplasia to osteosarcoma, in Mazabraud syndrome have been reported worldwide. The authors report the first case of osteosarcomatous transformation in a patient with Mazabraud syndrome in the Republic of Korea, focusing on imaging findings.
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