Anesth Pain Med.  2011 Jul;6(3):294-297.

Successful general anesthesia for cervical spine fusion in a patient with spondyloepiphyseal dysplasia congenita: A case report

Affiliations
  • 1Department of Anesthesiology and Pain Medicine, Incheon St. Mary's Hospital, College of Medicine, The Catholic University of Korea, Incheon, Korea. gkjw2000@yahoo.co.kr
  • 2Department of Orthopedic Surgery, Incheon St. Mary's Hospital, College of Medicine, The Catholic University of Korea, Incheon, Korea.

Abstract

Spondyloepiphyseal dysplasia congenita (SEDC) is a kind of skeletal dysplasia, inheritable condition. The clinical features of SEDC are dwarfism, myopia with or without retinal detachment, coxa vara, thoracic dysplasia with respiratory failure and laryngotracheal stenosis. A point of particular concern to anesthetists is odontoid hypoplasia which, combined with ligamentous laxity, leads to atlantoaxial instability. We report successful general anesthesia for cervical spine fusion of a patient with SEDC.

Keyword

Atlantoaxial instability; Spondyloepiphyseal dysplasia congenita

MeSH Terms

Anesthesia, General
Constriction, Pathologic
Coxa Vara
Dwarfism
Humans
Ligaments
Myopia
Osteochondrodysplasias
Respiratory Insufficiency
Retinal Detachment
Spine
Osteochondrodysplasias
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