J Korean Soc Radiol.  2013 Sep;69(3):239-242. 10.3348/jksr.2013.69.3.239.

Cervical Spinal Monostotic Fibrous Dysplasia: A Case Report

• Kim OH

• KMID: 2208807
• DOI: http://doi.org/10.3348/jksr.2013.69.3.239

Abstract

Monostotic fibrous dysplasia of the cervical vertebra is quite unusual. The author reports a case of monostotic fibrous dysplasia affecting the second cervical vertebra with descriptions from the CT, MR and bone scanning findings.

MeSH Terms

Fibrous Dysplasia, Monostotic
Magnetic Resonance Imaging
Spine

Figure

• 

  Fig. 1 Monostotic fibrous dysplasia of the C2 in a 42-year-old woman. A, B. Coronal (A) and sagittal (B) CT scan of C-spine reveal the irregular margined osteolytic lesion with peripheral bony sclerosis, without evidence of the bony cortical destructions, in C2 body. C-E. Sagittal MRI reveal the irregular margined osseous lesion incompletely surrounded by the rim of low signal intensity in the C2 body (arrows in C, D), showing low to intermediate SI on T1WI (C), heterogeneous mixed, low to high, SI on STIR image (D), and marked contrast enhancements (arrows in E) on Gd-T1WI (E) at the sites corresponding to the osteolytic areas of CT scan. F. Bone scan following administration of Tc-99m MDP reveal the focal tracer uptake in the upper cervical spine. Note no other skeletal tracer uptake in the whole body scan. G. Photomicrograph of surgical specimen shows classic microscopic appearance of fibrous dysplasia consisting of irregular immature trabeculae of woven bone with lack of osteoblastic rimming (arrowheads) in bland fibroblastic and collagenous matrix (arrows) (H&E stain, × 40). Note.-Gd = gadolineum, MDP = methylene diphosphonate, SI = signal intensity, STIR = short tau inversion recovery, T1WI = T1-weighted image

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