- Atypical hemolytic uremic syndrome and eculizumab therapy in children
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Kim SH, Kim HY, Kim SY
- KMID: 2452038
- Korean J Pediatr.
- 2018 Feb;61(2):37-42.
- doi: 10.3345/kjp.2018.61.2.37
Hemolytic uremic syndrome (HUS) is often encountered in children with acute kidney injury. Besides the well-known shiga toxin-producing Escherichia coli-associated HUS, atypical HUS (aHUS) caused by genetic complement dysregulation has... -
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- A case of atypical hemolytic uremic syndrome associated with the c.1273C>T mutation in the complement C3 gene
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Cho HJ, Kim JO, Huh JY, Park Y, Kim MG, Oh D
- KMID: 2353506
- Blood Res.
- 2016 Sep;51(3):210-213.
- doi: 10.5045/br.2016.51.3.210
No abstract available. -
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- Atypical Hemolytic Uremic Syndrome in a 13-year-old Lao Girl: A Case Report
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Kedsatha P, Cheong HI, Choi Y
- KMID: 2448161
- Child Kidney Dis.
- 2019 Apr;23(1):43-47.
- doi: 10.3339/jkspn.2019.23.1.43
Atypical hemolytic uremic syndrome (aHUS), a rare form of thrombotic microangiopathy, is distinguished from the typical form by the absence of a preceding verotoxin-producing Escherichia coli infection. Notably, aHUS occurs... -
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- Kidney Transplantation in Patients with Atypical Hemolytic Uremic Syndrome due to Complement Factor H Deficiency: Impact of Liver Transplantation
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Kim S, Park E, Min SI, Yi NJ, Ha J, Ha IS, Cheong HI, Kang HG
- KMID: 2399161
- J Korean Med Sci.
- 2018 Jan;33(1):e4.
- doi: 10.3346/jkms.2018.33.e4
BACKGROUND: Atypical hemolytic uremic syndrome (aHUS) is a rare disease that is often associated with genetic defects. Mutations of complement factor H (CFH) are the most common genetic defects that... -
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- Clinical Practice Guidelines for the Management of Atypical Hemolytic Uremic Syndrome in Korea
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Cheong HI, Jo SK, Yoon SS, Cho H, Kim JS, Kim YO, Koo JR, Park Y, Park YS, Shin JI, Yoo KH, Oh D
- KMID: 2468240
- J Korean Med Sci.
- 2016 Oct;31(10):1516-1528.
- doi: 10.3346/jkms.2016.31.10.1516
Atypical hemolytic uremic syndrome (aHUS) is a rare syndrome characterized by micro-angiopathic hemolytic anemia, thrombocytopenia, and acute kidney injury. The major pathogenesis of aHUS involves dysregulation of the complement system.... -
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- Prognostic utility of ADAMTS13 activity for the atypical hemolytic uremic syndrome (aHUS) and comparison of complement serology between aHUS and thrombotic thrombocytopenic purpura
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Oh J, Oh D, Lee SJ, Kim JO, Kim NK, Chong SY, Huh JY, Baker RI, on behalf of the Korean TTP Registry Investigators
- KMID: 2459388
- Blood Res.
- 2019 Sep;54(3):218-228.
- doi: 10.5045/br.2019.54.3.218
BACKGROUND: Atypical hemolytic uremic syndrome (aHUS) involves dysregulation of the complement system, but whether this also occurs in thrombotic thrombocytopenic purpura (TTP) remains unclear. Although these conditions are difficult to... -
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- Clinical characteristics and outcomes of thrombotic microangiopathy in Malaysia
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Yap YY, Sathar J, Law KB, Zulkurnain PAB, Edmund SC, Chang KM, Baker R
- KMID: 2451031
- Blood Res.
- 2018 Jun;53(2):130-137.
- doi: 10.5045/br.2018.53.2.130
BACKGROUND: Thrombotic microangiopathy (TMA) with non-deficient ADAMTS-13 (a disintegrin-like and metalloprotease with thrombospondin type 1 motif 13) outcome is unknown hence the survival analysis correlating with ADAMTS-13 activity is conducted... -
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