Korean J Gastroenterol.  2007 Oct;50(4):271-276.

A Case of Simple Type Caroli's Disease Confined to Right Lobe of the Liver

Affiliations
  • 1Department of Internal Medicine, Chungbuk National University College of Medicine, Cheongju, Korea. smpark@chungbuk.ac.kr
  • 2Department of Pathology, Chungbuk National University College of Medicine, Cheongju, Korea.
  • 3Department of Radiology and Surgery, Chungbuk National University College of Medicine, Cheongju, Korea.

Abstract

Caroli's disease is a rare congenital hepatobiliary disease characterized by multifocal segmental dilatation of intrahepatic bile ducts affecting all or parts of the liver. Two forms of Caroli's disease are described, the pure form and that associated with periportal fibrosis. The disease may diffusely affect the liver or be localized to one lobe or segment. Less than 20% of all reported cases of Caroli's disease are monolobar type. We report a case of simple type Caroli's disease confined to right lobe of the liver in a 22 year old man. He was admitted due to right upper abdominal pain and diagnosed by magnetic resonance cholangiopancreatography. He was treated with right hepatic lobectomy and recovered completely.

Keyword

Caroli's disease; Monolobar type; Right hepatic lobectomy

MeSH Terms

Adult
Bile Ducts, Intrahepatic/pathology
Caroli Disease/diagnosis/pathology/*surgery
Common Bile Duct/surgery
Diagnosis, Differential
Hepatectomy
Humans
Liver/*pathology
Magnetic Resonance Imaging
Male
Tomography, X-Ray Computed
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