J Korean Neurol Assoc.
2024 Nov;42(4):348-352. 10.17340/jkna.2024.0059.
Neuronal Intranuclear Inclusion Disease Presented with Acute Aphasia
- Affiliations
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- 1Department of Neurology, Dankook University Hospital, Cheonan, Korea
- 2Department of Neurology, Dankook University College of Medicine, Cheonan, Korea
- KMID: 2560991
- DOI: http://doi.org/10.17340/jkna.2024.0059
Abstract
- Neuronal intranuclear inclusion disease (NIID) is a rare disorder with slowly progressive neurodegeneration. Major clinical presentation is dementia, but some patients can have episodic symptoms. This is a rare case of NIID presented with acute aphasia. A 62-years-old male visited emergency room presenting with aphasia. On brain magnetic resonance imaging, a U-shaped diffusion high signal intensity lesion in bilateral frontal corticomedullary junction was observed. A skin biopsy showed intranuclear cytoplasmic inclusion bodies, so he was diagnosed as NIID.
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