Korean J Neuromuscul Disord.  2022 Dec;14(2):38-41. 10.46518/kjnmd.2022.14.2.38.

A Case Report of Sensory Guillain-Barré Syndrome with Prominent Autonomic Dysfunction in a Systemic Lupus Erythematosus Patient

• Kim YS
• Kim YS

• KMID: 2539420
• DOI: http://doi.org/10.46518/kjnmd.2022.14.2.38

Abstract

Sensory Guillain-Barré syndrome (GBS) is a rare heterogeneous subgroup of GBS characterized by the primary involvement of sensory neurons resulting in a distinctive clinical presentation. Sensory GBS usually occurs with acute and monophasic sensory symptoms, and no or minimal muscle weakness. Sensory GBS patient show hypo- or areflexia, distal paresthesia, and normal cerebrospinal fluid finding or albumino-cytologic dissociation which are suggesting that these conditions are a GBS variant. Autonomic dysfunctions have rarely been reported in sensory GBS patient presenting with postural hypotension, abnormal heart rate response to respiration. In this case, we demonstrate a patient with autonomic symptoms dominant sensory GBS in systemic lupus erythematosus.

Keyword

Guillain-Barré syndrome; Ataxia; Dysautonomia