J Korean Soc Radiol.  2021 Sep;82(5):1304-1309. 10.3348/jksr.2020.0181.

Undifferentiated Pleomorphic Sarcoma of the Small Intestine with Distant Endobronchial Metastasis Presenting as Intussusception: A Case Report

• Song SO
• Kim MS
• Lee KH
• Choi SJ

• KMID: 2520712
• DOI: http://doi.org/10.3348/jksr.2020.0181

Abstract

Undifferentiated pleomorphic sarcoma (UPS) is a high-grade soft tissue sarcoma that arises from mesenchymal tissue. Primary UPS of the small intestine is extremely rare, and only a few cases have been reported in the literature. Its presentation is usually nonspecific; however, it may occasionally present as intussusception with intermittent abdominal pain. It is a highly aggressive tumor with a propensity for early distant metastasis to the peritoneum, lymph nodes, other abdominal organs, lungs and brain. To our knowledge, there are no reported cases of endobronchial metastasis from small intestine UPS. We report a rare case of UPS of the small intestine with endobronchial metastasis presenting as intussusception.

Keyword

Soft Tissue Sarcoma; Small Intestine; Intussusception; Computed Tomography; X-Ray; Endobronchial Metastasis