Anat Cell Biol.  2020 Dec;53(4):509-511. 10.5115/acb.20.057.

Caudal regression syndrome and a pelvic kidney:case report

• Hage D
• Iwanaga J
• Dumont AS
• Tubbs RS

• KMID: 2509698
• DOI: http://doi.org/10.5115/acb.20.057

Abstract

Caudal regression syndrome (CRS) is a rare congenital variation. A high incidence of renal and genitourinary malformations has been observed in patients with CRS, with the most common being neurogenic bladder and renal agenesis. We report a rare case report documenting both CRS and a pelvic kidney found during a diagnostic magnetic resonance imaging. Although renal anatomy variants are found in patients with CRS, a pelvic kidney is normally not part of the constellation of findings in this malformation. As seen in our patient, a pelvic kidney should be considered in patients suspected of having CRS.

Keyword

Caudal regression syndrome; Pelvic kidney; Magnetic resonance imaging; Renal malformation; Renal malformation

Figure

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  Fig. 1 Plain abdominal X-ray showing hypoplasia of the distal sacrum.

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  Fig. 2 T1-weighted sagittal magnetic resonance imaging. Note the lower left kidney located in the midline with the ureter posteriorly and a large pelvic kidney.

Reference

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