J Korean Soc Radiol.  2020 Sep;81(5):1204-1209. 10.3348/jksr.2019.0119.

Undifferentiated Pleomorphic Sarcoma of the Thoracic Aorta Presenting with Ruptured Saccular Aneurysm: A Case Report

• Kim DW
• Kim YH
• Kang UR
• Cho JW
• Jang JS

• KMID: 2507429
• DOI: http://doi.org/10.3348/jksr.2019.0119

Abstract

Cases of undifferentiated pleomorphic sarcoma of the thoracic aorta are rare, and usually present with embolic events, renovascular hypertension, or back pain. Mural-based undifferentiated pleomorphic sarcomas that present as ruptured saccular aneurysms are extremely rare and are difficult to differentiate from mycotic aneurysms or penetrating atherosclerotic ulcers. Herein, we report a case of histopathologically proven undifferentiated pleomorphic sarcoma arising from the wall of the descending thoracic aorta that manifested as a mass after thoracic endovascular aortic repair for the treatment of a ruptured saccular aneurysm. We present findings obtained by CT and PET to provide helpful information for the accurate diagnosis and appropriate treatment of future cases.

Keyword

Sarcoma; Aortic Aneurysm; Computed Tomography; X-Ray; Positron Emission Tomography