J Korean Soc Radiol.  2019 Nov;80(6):1271-1275. 10.3348/jksr.2019.80.6.1271.

Absence of the Intrahepatic Inferior Vena Cava with Polysplenia Syndrome on Multidetector Computed Tomography: A Case Report

• Hwang S
• Kim JA

• KMID: 2464926
• DOI: http://doi.org/10.3348/jksr.2019.80.6.1271

Abstract

Various anomalies of the inferior vena cava (IVC) can arise from a failure in the normal embryogenic processes. Agenesis of the intrahepatic segment of the IVC with azygos continuation, which is caused by failure of formation of the right subcardinal-hepatic anastomosis, is a rare IVC anomaly. In this paper, we report a case of interrupted IVC with azygos vein continuation, combined with polysplenia, intestinal malrotation, and truncated pancreas, which was incidentally found on abdominal CT and thoracic aorta CT angiography.

MeSH Terms

Angiography
Aorta, Thoracic
Azygos Vein
Heterotaxy Syndrome*
Multidetector Computed Tomography*
Pancreas
Tomography, X-Ray Computed
Vena Cava, Inferior*

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