- Heterotaxy Syndrome
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Kim SJ
- KMID: 2297927
- Korean Circ J.
- 2011 May;41(5):227-232.
- doi: 10.4070/kcj.2011.41.5.227
Heterotaxy is defined as an abnormality where the internal thoraco-abdominal organs demonstrate abnormal arrangement across the left-right axis of the body. This broad term includes patients with a wide variety... -
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- Clinical Study on Asplenia and Polysplenia Syndrome
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Choi JY, Yun YS, Hong CY
- KMID: 1682810
- J Korean Pediatr Soc.
- 1989 May;32(5):653-658.
No abstract available. -
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- 2 Cases of Congenital Asplenia Syndrome
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Joo HS, Chu CH, Cho BS, Rhee KH, Chung SJ, Ahn CI
- KMID: 1698956
- J Korean Pediatr Soc.
- 1984 Feb;27(2):191-196.
No abstract available. -
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- Situs Ambiguous with Polysplenia of Macrosomia
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Jang WT, Kim HJ, Kim JS, Yoon HS
- KMID: 2409113
- Perinatology.
- 2018 Mar;29(1):52-56.
- doi: 10.14734/PN.2018.29.1.52
Situs ambiguous is a very rare disease with one or less per 10,000 newborns whose organs are not in normal position. It usually has spleen and heart malformations, and if... -
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- Diabetes mellitus due to agenesis of the dorsal pancreas in a patient with heterotaxy syndrome
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Jung JE, Hur JH, Jung MK, Kwon A, Chae HW, Kim DH, Kim HS
- KMID: 2383908
- Ann Pediatr Endocrinol Metab.
- 2017 Jun;22(2):125-128.
- doi: 10.6065/apem.2017.22.2.125
Heterotaxy syndrome (HS) is a congenital disorder resulting from an abnormal arrangement of visceral organs across the normal left-right axis in the embryonic period. HS is usually associated with multiple... -
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- Three cases of asplenia syndrome associated with congenital heart disease
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Yoo SJ, Han MC, Kim SH
- KMID: 2345357
- J Korean Radiol Soc.
- 1980 Dec;16(2):519-528.
- doi: 10.3348/jkrs.1980.16.2.519
No abstract available in English. -
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- A Case of Congenital Asplenia Syndrome
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Kim HS, Cho JS, Jim SK, Moon DS, Cho KS, Cho JD
- KMID: 1676907
- J Korean Pediatr Soc.
- 1987 Feb;30(2):218-222.
No abstract available. -
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- A Case of Unusual Visceral Heterotaxy Syndrome with Isolated Levocardia
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Jo DS, Jung SS, Joo CU
- KMID: 1826564
- Korean Circ J.
- 2013 Oct;43(10):705-709.
- doi: 10.4070/kcj.2013.43.10.705
Situs inversus of the abdominal organs in the presence of normally placed heart on the left side of the thorax is known as situs inversus with isolated levocardia. This rare... -
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- Absence of the Intrahepatic Inferior Vena Cava with Polysplenia Syndrome on Multidetector Computed Tomography: A Case Report
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Hwang S, Kim JA
- KMID: 2464926
- J Korean Soc Radiol.
- 2019 Nov;80(6):1271-1275.
- doi: 10.3348/jksr.2019.80.6.1271
Various anomalies of the inferior vena cava (IVC) can arise from a failure in the normal embryogenic processes. Agenesis of the intrahepatic segment of the IVC with azygos continuation, which... -
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- The Results of Extracardiac Fontan Operation in the Patients with Heterotaxy Syndrome
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Lim HG, Kim SJ, Lee CH, Kim WH, Hwang SW, Lee C, Oh SS, Baek MJ, Na CY, Kim JH, Seo HJ, Jung SC, Kim CW, Kim JS
- KMID: 2289132
- Korean J Thorac Cardiovasc Surg.
- 2005 Aug;38(8):529-537.
BACKGROUND: Historically the Fontan operation in patients with single ventricle and heterotaxy syndrome has been associated with high mortality because of systemic or pulmonary anomalous venous drainage, incompetent common atrioventricular... -
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- Total Anomalous Pulmonary Venous Return in Functional Single Ventricle and Postoperative Pulmonary Venous Obstruction: Contemporary Therapeutic Strategies for Right Atrial Isomerism
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Yun TJ
- KMID: 1946399
- J Korean Pediatr Cardiol Soc.
- 2005 Dec;9(2):264-271.
No abstract available. -
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- A case of fetal heterotaxy syndrome
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Chon SJ, Kim SY, Lee SP, Hwang BC, Son DW, Choi CH
- KMID: 1836751
- Korean J Obstet Gynecol.
- 2011 Oct;54(10):630-633.
- doi: 10.5468/KJOG.2011.54.10.630
Heterotaxy syndrome is a disorder that results in abnormal placement of organs. We report the prenatal diagnosis of complex cardiac abnormalities associated with left isomerism. A 32-year-old multigravida was referred... -
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- A Case of Corpus Callosun Agenesis with Situs Ambiguus
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Cheong K, Yoo J, Seo J, Rhee K, Chung Y
- KMID: 1683431
- J Korean Pediatr Soc.
- 1990 Jun;33(6):854-859.
No abstract available. -
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- Anomalies of Abdominal Organs in Polysplenia Syndrome: Multidetector Computed Tomography Findings
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Kim S, Lee YS, Jung JH
- KMID: 2152603
- J Korean Soc Radiol.
- 2016 Feb;74(2):114-122.
- doi: 10.3348/jksr.2016.74.2.114
Polysplenia syndrome is a rare situs ambiguous anomaly associated with multiple spleens and anomalies of abdominal organs. Because most of the minor anomalies do not cause clinical symptoms, polysplenia syndrome... -
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- A Case of Congenital Complete Heart Block
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Jeong DB, Rho YI, Moon KR, Park YB, Park SK
- KMID: 2188775
- J Korean Soc Neonatol.
- 1999 May;6(1):133-144.
In complete heart block(CHB), there is a complete failure of the atrial impulse leading into a ventricular response, the atria and ventricles beat independently, with the latter having a slower... -
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- Polysplenia Syndrome with Congenital Agenesis of Dorsal Pancreas Presenting as Acute Pancreatitis and the Role of Endoscopic Ultrasonography in Its Diagnosis
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Jeong JH, Kim GH, Song GA, Lee DG, Moon JY, Cheong JH, Kim S
- KMID: 1718466
- Korean J Gastroenterol.
- 2012 Jul;60(1):47-51.
- doi: 10.4166/kjg.2012.60.1.47
A 49-year-old female was admitted to our hospital for acute pancreatitis. The abdomen CT scan incidentally showed midline liver with hepatomegaly, centrally located gallbladder, pancreas truncation, right sided small bowel,... -
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- Aggressive Surgical Treatment for Complex Cardiac Anomalies Associated with Right Atrial Isomerism
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Hwang UD, Yun TJ, Jung SH, Jhang WK, Kim YH
- KMID: 1520035
- Korean J Thorac Cardiovasc Surg.
- 2007 Aug;40(8):569-573.
A 3 month old female baby, who had been diagnosed with right atrial isomerism associated with total anomalous pulmonary venous return (TAPVR), a functional single ventricle and major aortopulmonary collateral... -
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- Prenatal Diagnosis of Complete Atrioventricular Septal, Defect:Clinical Outcome of 35 Cases
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Yang HJ, Park HY, Kim IK, Ji EK, Choi YM, Hong SK
- KMID: 1592414
- J Korean Pediatr Cardiol Soc.
- 2002 Dec;6(2):182-187.
PURPOSE: Prenatal diagnosis of congenital heart disease has been made by fetal echocardiography and its clinical impact on the outcome of complete atrioventricular septal defect(AVSD) cases has been analysed. METHODS:... -
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- Asplenia(right atrial isomerism) diagnosed by prenatal ultrasonography: Report of One Case
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Yeon JE, Yoo YG, Kang EJ, Hur HK, Park DH, Kim KS, Hong SH, Moon HS
- KMID: 2269881
- Korean J Obstet Gynecol.
- 1999 Sep;42(9):2084-2087.
The syndromes of left atrial isomerism and right atrial isomerism, called polysplenia and asplenia syndromes, respectively, consist of congenital heart defects with disturbances in normal left right isometry, and the... -
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- Multidetector-Row CT Findings of a Preduodenal Portal Vein Associated with Polysplenic Syndrome in an Adult: A Case Report
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Song H, Lee SL, Ku YM, Chun CW
- KMID: 1439427
- J Korean Soc Radiol.
- 2012 Mar;66(3):279-282.
- doi: 10.3348/jksr.2012.66.3.279
Preduodenal portal vein (PDPV) is a rare developmental anomaly in which the portal vein runs at the ventral side of the duodenum instead of at an intrapancreatic location. Understanding of... -
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