J Korean Soc Radiol.  2010 Aug;63(2):103-105.

Unilateral Enophthalmos in Linear Scleroderma: A Case Report

• Cho SH
• Hwang HY
• Choi HY
• Kim HS

Abstract

Linear scleroderma is an uncommon subtype of localized scleroderma, which is characterized by a linear streak that crosses dermatomes and is associated with the tracking of fibrosis from the skin into deeper tissues, including muscle and fascia. A severe form of this condition sometimes causes growth atrophy of bone and supporting tissue in the affected area. Enophthalmos as a manifestation of linear scleroderma is very rare and occurs due to the replacement of orbital fat and muscle with collagen, which finally leads to atrophy of the affected orbit. This report introduces imaging findings of two cases of enophthalmos caused by linear scleroderma.

MeSH Terms

Atrophy
Collagen
Enophthalmos
Fascia
Fibrosis
Muscles
Orbit
Scleroderma, Localized
Skin
Track and Field
Collagen

Figure

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  Fig. 1 A, B. Axial 1A and Sagittal 1B enhancing orbital CT shows enophthalmos, a decreased amount of the orbital fat and a reduction in the size of the left orbit. The retrobulbar enhancing lesion suggests inflammatory tissue associated with scleroderma.

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  Fig. 2 A, B. Axial T1 2A and T2 2B weighted MR images demonstrate a depressed left eyeball, a decreased amount of orbital fat, and a reduction in the size of the left orbit. Linear low signal intensity lesions of left retrobular soft tissue on T1 weighted image is identified as involved inflammatory tissue.

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