Ann Surg Treat Res.  2018 Mar;94(3):162-165. 10.4174/astr.2018.94.3.162.

Laparoscopic hepatectomy for the treatment of Caroli's disease: a case report

• Chen CB
• Hu WD
• Zhao WW
• Gu YY
• Hou HW
• Pan Z

• KMID: 2405330
• DOI: http://doi.org/10.4174/astr.2018.94.3.162

Abstract

Caroli disease is a rare congenital disorder characterized by nonobstructive dilatation of intrahepatic ducts. In cases with symptomatic intrahepatic manifestations, treatment should correspond to the type with hepatic resection for localized disease and transplantation for diffuse forms. If possible, complete resection of the cysts can cure the symptoms and avoid the risk of malignancy. A 66-year-old woman presented to Wuxi Xishan People's Hospital with recurrent intermittent upper quadrant abdominal pain. Further examinations suggested the diagnosis of Caroli disease limited to the left hepatic lobe. She underwent laparoscopic hepatectomy. Pathological examination confirmed the diagnosis of Caroli disease, and no malignancy was found. There were no immediate complications and no long-term complications after one and one-half years of follow-up. Laparoscopic hepatectomy could be a feasible, safe treatment option for localized Caroli disease.

Keyword

Caroli disease; Cholecystectomy; Laparoscopy

MeSH Terms

Abdominal Pain
Aged
Caroli Disease*
Cholecystectomy
Congenital, Hereditary, and Neonatal Diseases and Abnormalities
Diagnosis
Dilatation
Female
Follow-Up Studies
Hepatectomy*
Humans
Laparoscopy

Figure

• 

  Fig. 1 CT findings. (A) Enhanced transverse CT reveals grape-like dilated left intrahepatic bile ducts (arrow) with middle hepatic vein close to capsule wall (arrowhead). (B) Sagittal plane of enhanced CT shows atrophic left lobe with dilated intrahepatic bile ducts and gallbladder calculus.

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  Fig. 2 Magnetic resonance cholangiopancreatography (MRCP) findings. MRCP revealed irregular intrahepatic bile duct dilatation of left lobe with obstructed left hepatic duct, while common bile duct and right intrahepatic bile duct are normal.

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  Fig. 3 Histopathologic findings showed congenital dilatation of intrahepatic bile ducts, confirming preoperative diagnosis of Caroli disease (H&E, x400).

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