Korean J Thorac Cardiovasc Surg.  2015 Oct;48(5):364-367. 10.5090/kjtcs.2015.48.5.364.

Emergency Quadrido-Bentall Procedure for Aortic Rupture in a Patient with Behcet's Disease

• Park SJ
• Lee JW
• Kim JB

• KMID: 2382288
• DOI: http://doi.org/10.5090/kjtcs.2015.48.5.364

Abstract

Cardiovascular involvement in cases of Behcet's disease is a rare but life-threatening condition, and prosthetic valve detachment is a frequent and serious complication attributable to Behcet's disease following the surgical repair of aortic regurgitation. We report the case of a patient with Behcet's disease presenting with contained aortic rupture around the aortic root. The patient had previously undergone aortic valve surgery three times due to recurrent prosthetic valve detachment. An emergency operation was performed, consisting of aortic root replacement (ARR) using a composite valved conduit and the replacement of the hemiarch. ARR may be an appropriate surgical option for patients with Behcet's disease in order to prevent recurrence of the disease.

Keyword

Aortic valve; Aortic valve insufficiency; Extracorporeal circulation; Behcet syndrome; Surgery

MeSH Terms

Aortic Rupture*
Aortic Valve
Aortic Valve Insufficiency
Behcet Syndrome
Emergencies*
Extracorporeal Circulation
Humans
Recurrence