J Rhinol.  2017 May;24(1):48-51. 10.18787/jr.2017.24.1.48.

A Case of Fibromyxoma of the Maxilla

• Lee DJ
• Chung YJ

• KMID: 2379790
• DOI: http://doi.org/10.18787/jr.2017.24.1.48

Abstract

Fibromyxoma is a rare mesenchymal tumor that is benign, but locally invasive. It is a slow-glowing painless tumor with the potential for extensile bony destruction and cortical expansion and shows a relatively high recurrence rate. Fibromyxoma is found predominantly in the jaw, with the mandible more frequently affected than the maxilla. We recently experienced a case of fibromyxoma originating from the maxilla in a 50-year-old woman who complained of swelling on the right side of her cheek. En bloc resection via a sublabial approach and middle meatal antrostomy were performed. A diagnosis of fibromyxoma was based on pathologic findings. No recurrence or locally residual lesion has been found during 2-years follow up. Therefore, we present this rare case with a review of the literature.

Keyword

Fibromyxoma; Maxilla

MeSH Terms

Cheek
Diagnosis
Female
Fibroma*
Follow-Up Studies
Humans
Jaw
Mandible
Maxilla*
Middle Aged
Recurrence

Figure

• 

  Fig. 1 Axial (A) and coronal (B and C) CT scans show that 3.8×3.5×3.3 cm non-enhancing low attenuated expansile cystic mass with bone erosion nature in the right maxillary sinus.

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  Fig. 2 Gross finding (cutting view in the middle) reveals a grayish gelatinous mass having a glistening mucoid appearance. The mass appears well circumscribed and encapsulated.

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  Fig. 3 Histological appearance of fibromyxoma shows that cellular myxoid lesion with bland stellate and spindle cell (A, H & E stain, ×200) and fibromyxoma cells are immunohistochemically positive for vimentin (B).

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