Ann Dermatol.  2010 Feb;22(1):110-113. 10.5021/ad.2010.22.1.110.

A Case of Recurrent Superficial Acral Fibromyxoma

• Goo J
• Jung YJ
• Kim JH
• Lee SY
• Ahn SK

• KMID: 2172054
• DOI: http://doi.org/10.5021/ad.2010.22.1.110

Abstract

Superficial acral fibromyxoma (SAFM) is a rare myxoid tumor that was first described in 2001. The presence of a very slow growing solitary tender mass in the subungual area is the typical clinical feature at presentation. Histopathologically, SAFM is composed of stellate cells in a myxocollagenous matrix with a poorly circumscribed margin. This tumor is thought to be benign, but its natural course is not fully understood. We describe a 15-year-old patient with recurrent SAFM and discuss the proper treatment and follow up.

Keyword

Recurrent; Superficial acral fibromyxoma; Treatment

MeSH Terms

Adolescent
Fibroma
Follow-Up Studies
Humans

Figure

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  Fig. 1 The tender, growing subungual lesion and the distorted nail plate. The right side of the nail plate looked pale because of the pressing margin of the tumor.

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  Fig. 2 (A) Poorly circumscribed dermal tumor with myxoid and fibrous areas (H&E, ×40). (B) Stellate or fibroblast-like cells showing a fascicular growth pattern (H&E, ×100). (C) Stellate cells with an elongated thin cytoplasm were noted in the collagenous and mucinous areas. Blood vessels proliferated focally. (H&E, ×200).

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  Fig. 3 A recurrent tumor was noted 1 year 8 months after the initial procedure.

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