Brain Tumor Res Treat.  2017 Apr;5(1):42-44. 10.14791/btrt.2017.5.1.42.

Fourth Ventricle Neurenteric Cyst Mimicking Hemangioblastoma

• Choe E
• Hwang K
• Choe G
• Kim CY

• KMID: 2378305
• DOI: http://doi.org/10.14791/btrt.2017.5.1.42

Abstract

This report presents a case of fourth ventricle neurenteric cyst (NE cyst) mimicking hemangioblastoma, which developed in a 50-year-old woman. A tiny enhancing mural portion of the fourth ventricle in MRI suggested that the cyst was hemangioblastoma, but pathological evidence showed that the cyst was in fact NE cyst in the fourth ventricle. In order to make proper decision on to what extent of surgical resection should be done, considering every possibility in differential diagnosis might be helpful. This case reports an unusual pathology in 4th ventricle, considering the patient's age, and demonstrates that a rarer disease may share radiological features of a common disease.

Keyword

Neurenteric cyst; Fourth ventricle; Hemangioblastoma

MeSH Terms

Diagnosis, Differential
Female
Fourth Ventricle*
Hemangioblastoma*
Humans
Magnetic Resonance Imaging
Middle Aged
Neural Tube Defects*
Pathology

Figure

• 

  Fig. 1 Preoperative images of patient. A: Transverse CT image of the patient's head. A cystic lesion is clearly visible at the fourth ventricle and the cerebellum. B: Axial T2 MR image of the patient's head. The white color of the cystic region shown in this image suggests that the cyst is filled with CSF-like fluid. C: Coronal T1 MR image shows a suspicious tiny enhancing mural portion at right inferior cystic wall (pointed by the arrow). CSF, cerebrospinal fluid.

• 

  Fig. 2 Histopathological examination of the surgical specimen. A: Hematoxylin and eosin staining (×400) of a cuboidal epithelial lining with a basement membrane. B: Epithelial cells staining (×200) positively for CK7.

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