J Korean Med Sci.  2017 May;32(5):880-884. 10.3346/jkms.2017.32.5.880.

A Case of Cap Polyposis with Epidermal Nevus in an Infant

• Kim SC
• Kang MJ
• Jeong YJ
• Hwang PH

• KMID: 2375092
• DOI: http://doi.org/10.3346/jkms.2017.32.5.880

Abstract

Cap polyposis is extremely rare in children. We report a case of an 11-month-old male infant who visited our hospital because of rectal prolapse and small amount of hematochezia lasting several days. He also had an epidermal nevus in the sacral area. Colonoscopy showed erythematous, multilobulated, circumferential, polypoid lesions with mucoid discharge from the rectum. He was diagnosed with cap polyposis by endoscopy and histologic examination. He was treated with surgical resection, and was closely followed up. In the relevant literature, there is no report of cap polyposis in an infant. We report the first case of cap polyposis in the youngest infant.

Keyword

Cap Polyposis; Epidermal Nevus; Hematochezia

MeSH Terms

Child
Colonoscopy
Endoscopy
Gastrointestinal Hemorrhage
Humans
Infant*
Male
Nevus*
Rectal Prolapse
Rectum

Figure

• 

  Fig. 1 This picture shows asymmetric, bright, brown colored, diffuse groups of verrucous plaque, and an elevated macular epidermal nevus located in the lower back and sacral area.

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  Fig. 2 CT image shows well-enhanced, multiple polypoid lesions about 1 cm in size located at 5 cm above the anal verge. Multiple lymph node enlargement was noted. CT = computed tomography.

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  Fig. 3 Barium enema study shows multilobulated mass-like mucosal lesions in the recto-anal area. There was no evidence of mucosal destruction or obstruction from the rectum to the ascending colon.

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  Fig. 4 Multilobulated, 4–6 cm in size polypoid groups were seen from the anus to the proximal rectum on colonoscopic view.

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  Fig. 5 Hyperplastic crypts covered with calcified granulation tissue were revealed on histologic examination (H & E, ×100). H & E = hematoxylin and eosin.

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  Fig. 6 About 1-cm in size small remnant mucosal polypoid lesions were seen at the inner anus on follow-up endoscopy.

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