J Clin Neurol.  2016 Jan;12(1):115-116. 10.3988/jcn.2016.12.1.115.

Neurological Involvement in Erdheim-Chester Disease

• Alvarez-Alvarez M
• Macias-Casanova R
• Fidalgo-Fernandez MA
• Miramontes Gonzalez JP

• KMID: 2364928
• DOI: http://doi.org/10.3988/jcn.2016.12.1.115

Abstract

No abstract available.

MeSH Terms

Erdheim-Chester Disease*

Figure

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  Fig. 1 Brain MRI. A: An axial, T1-weighted cranial MRI image obtained after administering intravenous contrast medium, the arrow point the epidural enhancement on the frontal lobe. B: A coronal, T1-weighted cranial MRI image showing an infiltrating-like lesion on the left anterior cranial fossa with involvement of the apex, sphenoid fissure, and cavernous sinus. A polypoid lesion on the left nasal fossa can also be seen.

Reference

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2. Mazor RD, Manevich-Mazor M, Shoenfeld Y. Erdheim-Chester disease: a comprehensive review of the literature. Orphanet J Rare Dis. 2013; 8:137.

3. Perez A, Crahes M, Laquerrière A, Proust F, Derrey S. Neurological form of Erdheim-Chester disease: case report and review of the literature. Neurochirurgie. 2014; 60:316–320.

4. Cuello-Oderiz C, Pigretti S, Patrucco L. [Neurological onset of Erdheim-Chester disease]. Rev Neurol. 2014; 59:572–574.