Korean J Pediatr.  2016 Nov;59(Suppl 1):S145-S148. 10.3345/kjp.2016.59.11.S145.

Posterior reversible encephalopathy syndrome caused by presumed Takayasu arteritis

• Lee KW
• Lee ST
• Cho H

• KMID: 2362277
• DOI: http://doi.org/10.3345/kjp.2016.59.11.S145

Abstract

Takayasu arteritis (TA) is a chronic inflammatory disease of unknown etiology that affects mainly the aorta, main aortic branches, and pulmonary arteries. Diverse neurological manifestations of TA have rarely been reported in children. Posterior reversible encephalopathy syndrome (PRES) is a neuroradiological condition that presents with headache, seizure, visual disturbances, and characteristic lesions on imaging. Inflammatory condition and severe hypertension in TA can cause PRES. We report of a 5-year-old girl with presumed TA who presented with PRES and chronic total occlusion in the renal artery. The findings on magnetic resonance imaging suggested PRES. Left nephrectomy was performed for total occlusion of the left renal artery, and the confirmatory diagnosis of TA was based on the pathologic findings of the renal artery.

Keyword

Posterior reversible encephalopathy syndrome; Takayasu arteritis; Child

MeSH Terms

Aorta
Child
Child, Preschool
Diagnosis
Female
Headache
Humans
Hypertension
Magnetic Resonance Imaging
Nephrectomy
Neurologic Manifestations
Posterior Leukoencephalopathy Syndrome*
Pulmonary Artery
Renal Artery
Seizures
Takayasu Arteritis*