Ann Dermatol.  1992 Jul;4(2):103-107. 10.5021/ad.1992.4.2.103.

Phakomatosis Pigmentovascularis

• Oh CK
• Moon DC
• Kwon KS
• Chung TA

• KMID: 2361750
• DOI: http://doi.org/10.5021/ad.1992.4.2.103

Abstract

Phakomatosis pigmentovascularis was first described in 1947 as a distinctive association of cutaneous hemangioma and pigmentary nevi by Ota et al. We describe a 7-year-old boy who, since birth, had three kinds of discolored patches over the various parts of the body: blue spots (dermal melanocytic nevi), reticulated reddish patches (nevus flammeus), and hypopigmented macules (nevus anemicus). No systemic disease was found.

Keyword

Dermal melanocytic nevi; Nevus anemicus; Nevus flammeus; Phakomatosis Pigmentovascularis

MeSH Terms

Child
Hemangioma
Humans
Male
Neurocutaneous Syndromes*
Nevus
Parturition
Port-Wine Stain