Korean J Dermatol.  1994 Aug;32(4):707-712.

A Case of Phakomatosis Pigmentovascularis Associated with Leg - Length Discrepancy

• Choi JY
• Lee MH
• Haw CR

Abstract

Phakomatosis pigmentovascularis was first reported in 1947 as adiease complex with a distinct association of pigmentary nevus such as nevus of Ota, nevus of Ito, bilon golian spots, nevus spilus and cutaneous hemangioma such as nevus flammeus, which wss assoeisted with systemic organ involvment, We report a case of phakomatosis pigmentovascularis in a 11-year-old girl who had nevus flammeus, nevus spilus, and n.evus of Ota over various parts of her bo by since birth. She was also associated with leg-length discrepancy, but other systemic involvement was absent,

Keyword

Leg Length Discrepancy; Phakomatosis Pigmentovascularis

MeSH Terms

Child
Female
Hemangioma
Humans
Leg*
Neurocutaneous Syndromes*
Nevus
Nevus of Ota
Parturition
Port-Wine Stain