J Korean Radiol Soc.  1987 Apr;23(2):328-332. 10.3348/jkrs.1987.23.2.328.

Intralobar pulmonary sequestration with aberrant systemic artery - pulmonary vein fistula

• Lee YC
• Lee EH
• Nam MH
• Jeon SC
• Seo HS
• Hahm CK
• Lee KH

• KMID: 2359646
• DOI: http://doi.org/10.3348/jkrs.1987.23.2.328

Abstract

Intralobar pulmonary sequestration combined with aberrant systemic a tery-pulmonary vein fistula is rarecongenital malformation. Authors experienced a case of intralobar pulmonary sequestration combined witharteriovenous fistula in left lower lung. The patient was 8 year-old male whose complaint was dyspnea on exertion. The continuous murmur was heard over the left posterior chest wall. The chest film showed multiple tortuousbanching tubular shadows in the left lower lung field and dilated pulmonary vein at the infrahilar area. Thoracicaortogram showed that aberrant systemic artery originated from lower thoracic aorta and the arterial blood drainedinto left atrium directly through dilated left lower pulmonary vein. Left pulmonary arteriogram revealed thatthere was no vascular supply in the posterior basal segment of left lower lobe. At the time of operation,pulmonary sequestration was located in the posterior basal segment of left lower lobe and enveloped by the samevisceral pleura. A segmentectomy of left lower lobe with ligation of aberrant vessels was performed.

MeSH Terms

Aorta, Thoracic
Arteries*
Bronchopulmonary Sequestration*
Dyspnea
Fistula*
Heart Atria
Humans
Ligation
Lung
Male
Mastectomy, Segmental
Pleura
Pulmonary Veins*
Thoracic Wall
Thorax
Veins