Korean J Otorhinolaryngol-Head Neck Surg.
2016 Oct;59(10):742-745. 10.3342/kjorl-hns.2016.59.10.742.
A Case of Respiratory Arrest after Tonsillectomy and Adenoidectomy Surgery in a Patient with Rubinstein-Taybi Syndrome
- Affiliations
-
- 1Department of Otolaryngology, Asan Medical Center, University of Ulsan College of Medicine, Seoul, Korea. entysc@gmail.com
- 2Department of Otorhinolaryngology-Head and Neck Surgery, Hongik Hospital, Seoul, Korea.
- KMID: 2356329
- DOI: http://doi.org/10.3342/kjorl-hns.2016.59.10.742
Abstract
- Rubinstein-Taybi syndrome (RTS) is a rare autosomal dominant disorder characterized by mental and growth retardation, craniofacial, vertebral, ocular and cardiac anomalies, gastro-esophageal reflux, and difficult airway management. Patients with this syndrome can also experience upper airway obstruction during sleep, which is caused by hypotonia and the abnormal anatomy of the oropharynx and airways, and become susceptible to obstructive sleep apnea. In our case, respiratory arrest developed in an RTS patient who had undergone Tonsillectomy and Adenoidectomy (T&A) surgery. It is the first report of respiratory arrest after T&A surgery in a young child with RTS.
