Ann Dermatol.  2015 Jun;27(3):353-354. 10.5021/ad.2015.27.3.353.

Phacomatosis Pigmentovascularis Type Vb in a Three-Year Old Boy

• Jun HJ
• Kim SM
• Cho SH
• Lee JD
• Kim HS

• KMID: 2352520
• DOI: http://doi.org/10.5021/ad.2015.27.3.353

Abstract

No abstract available.

MeSH Terms

Humans
Male
Neurocutaneous Syndromes*

Figure

• 

  Fig. 1 (A~C) Reticulated, mottled, marble-like erythema on the face and arms, reticulated brown patches on the legs. In addition, bluish-grey patches are seen on the trunk and thighs. (D) The full leg X-ray shows discrepancy in length between the right and left leg.

• 

  Fig. 2 (A) Increased melanin pigment in the basal layer and dilation of capillary in the dermis (H&E, ×100). (B) Increased melanin pigment in the basal layer and scattered spindle-shaped melanocytes with melanin pigment in the dermis (H&E, ×100).

Reference

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2. Larralde M, Santos-Muñoz A, Rodríguez Cáceres M, Ciardiullo A. Phacomatosis pigmentovascularis type Va in a 3-month old. Pediatr Dermatol. 2008; 25:198–200.

3. Cifuentes L, Kollmar A, Ring J, Mempel M. Phacomatosis cesiomarmorata in an 8-month-old infant. Int J Dermatol. 2009; 48:1110–1112.

4. Smith JR, Moore MM, Stetson CL. JAAD grand rounds quiz. Red, purple, and brown skin lesions in a 2-month-old boy. Phakomatosis pigmentovascularis type V. J Am Acad Dermatol. 2012; 66:341–342.

5. Li TH, Chen TH, Lin HS, Liou CW, Liu JS, Chen SS, et al. Uncoupling of protein C and antithrombin III activity in cerebral ischemia patients associated with cutis marmorata. Acta Neurol Taiwan. 2008; 17:233–238.