Ann Dermatol.  2015 Jun;27(3):353-354. 10.5021/ad.2015.27.3.353.

Phacomatosis Pigmentovascularis Type Vb in a Three-Year Old Boy

Affiliations
  • 1Department of Dermatology, Incheon St. Mary's Hospital, College of Medicine, The Catholic University of Korea, Seoul, Korea. hazelkimhoho@gmail.com

Abstract

No abstract available.


MeSH Terms

Humans
Male
Neurocutaneous Syndromes*

Figure

  • Fig. 1 (A~C) Reticulated, mottled, marble-like erythema on the face and arms, reticulated brown patches on the legs. In addition, bluish-grey patches are seen on the trunk and thighs. (D) The full leg X-ray shows discrepancy in length between the right and left leg.

  • Fig. 2 (A) Increased melanin pigment in the basal layer and dilation of capillary in the dermis (H&E, ×100). (B) Increased melanin pigment in the basal layer and scattered spindle-shaped melanocytes with melanin pigment in the dermis (H&E, ×100).


Cited by  1 articles

A Case of Phacomatosis Pigmentovascularis Type IIa in a Korean Infant
Jae Won Ha, Ji Eun Hahm, So Eun Park, Jin Yong Lee, Chul Woo Kim, Sang Seok Kim
Ann Dermatol. 2017;29(5):638-639.    doi: 10.5021/ad.2017.29.5.638.


Reference

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