J Korean Neurol Assoc.  2014 Nov;32(4):285-288. 10.0000/jkna.2014.32.4.285.

Progressive Moyamoya Syndrome Associated with Paroxysmal Nocturnal Hemoglobinuria

• Ryu SG
• Lee SJ

• KMID: 2343555
• DOI: http://doi.org/10.0000/jkna.2014.32.4.285

Abstract

A 31-year-old female with paroxysmal nocturnal hemoglobinuria (PNH) presented with left hemiparesis. One year prior to this presentation she had been diagnosed with bihemispheric cerebral infarctions associated with moyamoya syndrome. During her current presentation, MRI revealed acute infarction of the right hemisphere and MRA revealed occlusion of the right internal carotid artery (ICA), and aggravation of the preexisting stenosis of the contralateral ICA and ipsilateral posterior cerebral artery compared to the previous MRA. We report herein a case of progressive moyamoya syndrome associated with PNH.

Keyword

Moyamoya syndrome; Paroxysmal nocturnal hemoglobinuria; Progression

MeSH Terms

Adult
Carotid Artery, Internal
Cerebral Infarction
Constriction, Pathologic
Female
Hemoglobinuria, Paroxysmal*
Humans
Infarction
Magnetic Resonance Imaging
Moyamoya Disease*
Paresis
Posterior Cerebral Artery