J Korean Neurol Assoc.  2002 Sep;20(5):568-570.

Two Cases of Evans Myopathy in a Family

• Cho JH
• Jung YK
• Kim SM
• Sunwoo IN

Abstract

Evans myopathy is a type of malignant hyperthermia showing characteristic distribution of myopathic changes. We present two cases of Evans myopathy, father and his son in a family. Five members of this family expired during ane sthesia and surgery and two of these cases were reported as the malignant hyperthermia. The muscle pathology shows moth-eaten appearance with or without unstained cores in NADH-TR stain and its difference between the father and his son is suggestive of rather progressive myopathy than static one. s

Keyword

Evans myopathy; Malignant hyperthermia

MeSH Terms

Fathers
Humans
Malignant Hyperthermia
Muscular Diseases*
Pathology