J Korean Child Neurol Soc.  2007 Nov;15(2):216-219.

Prolonged Survival of an Adult with Hydranencephaly

Affiliations
  • 1Department of Pediatrics, College of Medicine, Inje University, Busan, Korea. htg6700@chol.com
  • 2Department of Neurology, College of Medicine, Inje University, Busan, Korea.

Abstract

Hydranencephaly is a rare condition in which the brain's cerebral hemispheres are absent and replaced by sacs filled with cerebrospinal fluid. The prognosis for children with hydranencephaly is generally poor, so many children with this disorder die before the age of 1 year. We experienced a patient with hydranencephaly who showed prolonged survival until age of 22 years. To our limited knowledge, this case may be the longest survival of a patient with hydranencephaly in the world.

Keyword

Hydranencephaly; Survival; Prolonged; Adult

MeSH Terms

Adult*
Cerebrospinal Fluid
Cerebrum
Child
Humans
Hydranencephaly*
Prognosis
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