J Korean Child Neurol Soc.  2009 Nov;17(2):242-246.

A Case of Late Onset Atypical Craniosynostosis

• Kim KR
• Seok LJ
• Lee JS

Abstract

Craniosynostosis is a congenital deformity causing disorder in the growth of the skull and brain parenchyma, resulting from the fusion of the cranial sutures of calvaria or basilar before birth or within a few months after birth. In most cases it is diagnosed just after birth. However, some cases of vague diagnoses were reported, which was due to the late onset age, and the absence of typical symptoms and typical radiological findings. We make a report of a case in which the three-dimensional CT was helpful in making a diagnosis of a patient with minimal forms of craniosynostosis having minimal cranial deformities revealing just late onset raised intracranial pressure, along with the investigation of medical literature.

Keyword

Late-onset craniosynostosis; Pseudotumor cerebri

MeSH Terms

Age of Onset
Brain
Congenital Abnormalities
Cranial Sutures
Craniosynostoses
Humans
Intracranial Pressure
Parturition
Pseudotumor Cerebri
Skull