J Korean Soc Pediatr Endocrinol.  2005 Jun;10(1):71-75.

Otologic Evaluation in Children with Turner Syndrome

• Kim JS
• Kim SR
• Chung WY

Abstract

PURPOSE
Patients with Turner syndrome have been frequently suspected to have associated various otologic disorders and hearing loss. The purpose of this study was to evaluate the otologic problems in children with Turner Syndrome.
METHODS
Twenty patients aged 5 to 20 years who were diagnosed as Turner syndrome were evaluated audiologically.
RESULTS
Five subjects (25.0%) had previous histories of otitis media. An audiological examination was performed for all subjects and revealed normal hearing in 13 patients (65.0%), unilateral hearing loss in 3 patients (15.0%) and bilateral hearing loss in 4 patients (20.0%). Type of the hearing loss was conductive in 3 ears (7.5%), mixed in 2 ears (5.0%) and sensorineural in 6 ears (15.0%). Degree of hearing loss was mild in 9 ears, moderate in 1 ear and moderately severe in 1 ear. The incidence of hearing loss according to the karyotype revealed 10 ears (41.7%) in total deletion of Xp but only 1 ear (6.3%) in partial deletion of Xp.
CONCLUSION
Our results demonstrated that the otitis media and hearing loss were one of the common findings in children with Turner syndrome. These results emphasize the importance of regular otological examinations and audiological evaluation in children with Turner syndrome for quality of life.

Keyword

Turner syndrome; Hearing loss; Otitis media

MeSH Terms

Child*
Ear
Hearing
Hearing Loss
Hearing Loss, Bilateral
Hearing Loss, Unilateral
Humans
Incidence
Karyotype
Otitis Media
Quality of Life
Turner Syndrome*