Tuberc Respir Dis.  2006 Oct;61(4):403-406.

A Case of Tracheobronchomegaly with Pneumonia

• Joo KR
• Oak JH
• Lee SE
• Jang ST
• Kim SK
• Lee SH
• Song JS
• Park SH
• Moon HS
• Lee BY
• Kim HS

Abstract

A 66-years-old man was refered to our hospital because of cough, sputum, chill and fever. Enlargement of the trachea and main bronchi on radiography and bronchoscopy is compatible with Mounier-Kuhn syndrome. Mounier-Kuhn syndrome or tracheobronchomegaly is a rare disorder of uncertain etiology, characterized by marked dilatation of the trachea and major bronchi. This syndrome is associated with tracheal diverticulosis, bronchiectasis and recurrent respiratory tract infection. We report a rare case of Mounier-Kuhn syndrome with pneumonia and literature reviews.

Keyword

Mounier-Kuhn syndrome; Tracheobronchomegaly

MeSH Terms

Bronchi
Bronchiectasis
Bronchoscopy
Cough
Dilatation
Diverticulum
Fever
Pneumonia*
Radiography
Respiratory Tract Infections
Sputum
Trachea
Tracheobronchomegaly*

Figure

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  Figure 1 Chest X-ray shows ill-defined infiltrations in the right lower lobe. Dilatation of trachea and both bronchi are noted.

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  Figure 2 Chest CT scan in axial plane at the level of aortic arch shows dilatation of trachea, septation(arrowhead) in trachea and adjacent diverticula(arrow)(A). Ill-defined consolidation and small nodules are noted in right lower lobe(B).

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  Figure 3 Chest CT scan in coronal plane shows tracheomegaly and bronchomegaly(A). In three dimensional reconstruction CT bronchogram, anterior view(B) and lateral view(C) show diverticula(arrowhead).

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  Figure 4 Bronchoscopy shows the a divercitulum in posterior wall of trachea at the level of 5cm below vocal cord. There was some secretions in this diverticulum(A). This secretions were disappeared after bronchoscopic suction(B). This images were reconstructed by CT virtual bronchoscopy(C). Arrow points this diverticulum(C).

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